Perivascular epithelioid tumor (PEComa) of the falciform/ broad ligament.

نویسندگان

  • Janusz Ryś
  • Kazimierz Karolewski
  • Jacek Pudełek
  • Anna Kruczak
  • Anna Wasilewska
  • Maria Vogelgesang
  • Zbigniew Kojs
چکیده

PEComas localized in the region of falciform ligament and broad ligament are exceedingly rare. Most of them are built of spindle neoplastic cells. We report a case of epithelioid PEComa of the falciform ligament and/or broad ligament. There is only one report of such neoplasm in English-language literature. Histologically, the tumor was composed of nests of epithelioid clear cells stained positively for vimentin, HMB45, and SMA. Because of morphological features of the tumour (4 mitoses /20HPF, focal necrosis, and vascular invasion) we assess the neoplasm as potentially malignant.

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عنوان ژورنال:
  • Polish journal of pathology : official journal of the Polish Society of Pathologists

دوره 59 4  شماره 

صفحات  -

تاریخ انتشار 2008